Abstract: AIM: To review the clinical experience in the treatment of congential aneurysm of sinus of Valsalva and to investigate the surgical focal point. METHODS: Thirty patients with congenital aneurysm of sinus of Valsalva were operated on from November 1997 to December 2007. RESULTS: One patient, undergoing repair of aneurysm and ventricular septal defect and aortic valve replacement, died unexpectedly from ventricular fibrillation at the third postoperative day. One patient, undergoing aortic valvuloplasty, had mild aortic valve insufficiency postoperatively and developed into medium aortic valve insufficiency 3 years later. Cardiac function is currently NYHA class III. One case was lost to follow-up. The rest of the 27 patients were followed-up from 2 months to 10 years. Cardiac function of 20 patients was reported as NYHA class I and seven patients were reported as class II. CONCLUSION: Surgery for aortic sinus aneurysm should be performed as early as possible. Associated abnormalities must be corrected. Long-term results are associated with proper treatment of aortic valve regurgitation.